eprintid: 20193 rev_number: 12 eprint_status: archive userid: 1589 dir: disk0/00/02/01/93 datestamp: 2016-02-24 13:47:34 lastmod: 2024-05-17 16:41:07 status_changed: 2016-02-24 13:47:34 type: article metadata_visibility: show creators_name: Droste, Annette S. creators_name: Rohde, David creators_name: Völkers, Mirko creators_name: Filusch, Arthur creators_name: Bruckner, Thomas creators_name: Borst, Mathias Maximilian creators_name: Katus, Hugo A. creators_name: Meyer, F. Joachim title: Endothelin receptor antagonist and airway dysfunction in pulmonary arterial hypertension subjects: ddc-610 divisions: i-910100 divisions: i-911800 abstract: Background: In idiopathic pulmonary arterial hypertension (IPAH), peripheral airway obstruction is frequent. This is partially attributed to the mediator dysbalance, particularly an excess of endothelin-1 (ET-1), to increased pulmonary vascular and airway tonus and to local inflammation. Bosentan (ET-1 receptor antagonist) improves pulmonary hemodynamics, exercise limitation, and disease severity in IPAH. We hypothesized that bosentan might affect airway obstruction. Methods: In 32 IPAH-patients (19 female, WHO functional class II (n = 10), III (n = 22); (data presented as mean ± standard deviation) pulmonary vascular resistance (11 ± 5 Wood units), lung function, 6 minute walk test (6-MWT; 364 ± 363.7 (range 179.0-627.0) m), systolic pulmonary artery pressure, sPAP, 79 ± 19 mmHg), and NT-proBNP serum levels (1427 ± 2162.7 (range 59.3-10342.0) ng/L) were measured at baseline, after 3 and 12 months of oral bosentan (125 mg twice per day). Results and Discussion: At baseline, maximal expiratory flow at 50 and 25% vital capacity were reduced to 65 ± 25 and 45 ± 24% predicted. Total lung capacity was 95.6 ± 12.5% predicted and residual volume was 109 ± 21.4% predicted. During 3 and 12 months of treatment, 6-MWT increased by 32 ± 19 and 53 ± 69 m, respectively; p < 0.01; whereas sPAP decreased by 7 ± 14 and 10 ± 19 mmHg, respectively; p < 0.05. NT-proBNP serum levels tended to be reduced by 123 ± 327 and by 529 ± 1942 ng/L; p = 0.11). There was no difference in expiratory flows or lung volumes during 3 and 12 months. Conclusion: This study gives first evidence in IPAH, that during long-term bosentan, improvement of hemodynamics, functional parameters or serum biomarker occur independently from persisting peripheral airway obstruction. date: 2009-12-30 publisher: BioMed Central id_scheme: DOI ppn_swb: 1655995804 own_urn: urn:nbn:de:bsz:16-heidok-201938 language: eng bibsort: DROSTEANNEENDOTHELIN20091230 full_text_status: public publication: Respiratory Research volume: 10 number: 129 place_of_pub: London pagerange: 1-7 issn: 1465-993X citation: Droste, Annette S. ; Rohde, David ; Völkers, Mirko ; Filusch, Arthur ; Bruckner, Thomas ; Borst, Mathias Maximilian ; Katus, Hugo A. ; Meyer, F. Joachim (2009) Endothelin receptor antagonist and airway dysfunction in pulmonary arterial hypertension. Respiratory Research, 10 (129). pp. 1-7. ISSN 1465-993X document_url: https://archiv.ub.uni-heidelberg.de/volltextserver/20193/1/12931_2009_Article_843.pdf